Pyknodysostosis – Complications After Dental Extraction
Bahadun J., and Nik Hussien N.N. (Nik Noriah Nik Hussein), and Yunus N.N.N., (2007) Pyknodysostosis – Complications After Dental Extraction. Annals of Dentistry, 14 (1). 26p.. ISSN 0128-7532 Full text not available from this repository. Official URL: http://ejum.fsktm.um.edu.my/ArticleInformation.aspx?ArticleID=529 AffiliationsSarawak General Hospital. Dental Consultant Clinic University of Malaya. Faculty of Medicine. Dept. of Children’s Dentistry and Hospital Kuala Lumpur. Dept. of Paediatric Dentistry AbstractPyknodysostosis is a rare sclerosing bone disorder with autosomal recessive mode of inheritance. The condition is characterized by continuous bone deposition without physiological resorption, occurring mainly in the trabecular and not the cortical bone. The skeletal features include short stature, brachycephaly, open cranial sutures and fontanelles, diffuse osteosclerosis and obtuse mandibular angles. Among the oral features observed were grooved or furrowed palate and disturbances in eruption and exfoliation of teeth. Multiple fractures of long bones and osteomyelitis of the jaw are frequent complications. These are attributed to the increased brittleness and reduced vascularity of the bone as a result of continuous endosteal bone deposition. Treatment is usually successful with surgical management and sustained bactericidal antibiotic therapy, although hyperbaric oxygen has been recommended as adjunct treatment in the more refractory form. Repository Staff Only: item control page
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